Drs.
Luis Cárdenas M, Claudia Trincado , Gabriela Enriquez G, Paulina
Doggenweiler F,
Mónica Hinrichsen M, Pilar Soler O.
1. Unidad de Ecocardiografía
Hospital Luis Calvo Mackenna
2. Becado Centro Cardiovascular Hospital Luis Calvo Mackenna
3. Becado de Pediatría Hospital Luis Calvo Mackenna
4.Cardiólogo Unidad de Ecocardiografía Hospital Luis Calvo
Mackenna
Abstract
We describe the morphologic variabilty and fetal diagnosis in pulmonary
atresia with intact ventricular septum, within a chilean pediatric cardiovascular
center.
An uncommon disease, that shows considerable morphologic heterogeneity,
and with no local reports about this topic.
We studied a consecutive series of 28 cases, in a five year period (1997-2002),
at the Luis Calvo Mackenna Cardiovascular center.
Morphologic features of each case were evaluated by direct review of the
echocardiograms, angiocardiograms and from surgical reports. Among 28
infants, atresia was membranous in 82% and muscular in 18%. Right ventricle
was bipartite in 30%, unipartite in 6% and tripartite in 64% of cases.
Coronary arterial abnormalities were identified in 36%, and right ventricular
dependent coronary circulation in 7,1%. Median tricuspid annulus valvar
size was -3.
Fetal diagnosis was made in six of the 28 cases (21,4%) .In all of these
prenatally diagnosed patients arrengements were made in order for the
delivery to be fullfilled near by a cardiovascular center.
This study shows data about the morphologic diversity and efforts on early
fetal diagnose made in our country, in order to asses this uncommon disease.
Key words: Atresia, Neonatal, Pulmonary, Morphology.
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Ecocardiografía
fetal en corte de cuatro cavidades, se aprecia VD hipoplásico.
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Ventriculografía derecha, muestra llene de coronarias a partir de fístulas desde VD. |
Cárdenas L y cols. Atresia pulmonar con septum ventricular intacto espectro morfológico y diagnóstico prenatal. Rev Chil Ultrasonog 2002; 5: 68 - 73.
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Volver al sumario, volumen 5, número 3 |